MIME-Version: 1.0 Content-Type: multipart/related; boundary="----=_NextPart_01C56DF5.994A5DD0" هذا المستند عبارة عن صفحة ويب أحادية الملف, والمعروف أيضاً بملف أرشيف ويب. إذا كنت ترى هذه الرسالة، فإن برنامج الاستعراض أو المحرر لا يعتمد ملفات أرشيف ويب. يُرجى تحميل برنامج استعراض يعتمد أرشيف ويب, مثل Microsoft Internet Explorer. ------=_NextPart_01C56DF5.994A5DD0 Content-Location: file:///C:/D91A186E/DRMOUSSABARQAWI-ACTUALSITUATIOPNOFTHALASSEMIAINJORDAN.htm Content-Transfer-Encoding: quoted-printable Content-Type: text/html; charset="us-ascii" ACTUAL SITUATIOPN OF THALASSEMIA IN JORDAN

يحتوي هذا العرض التقديمي عل= 09; محتويات ربم= 75; يتعذر على المستعر= 90; إظهارها بصورة صحيحة. لقد تم إنشاء هذا العرض التقديمي ليعمل بشكله = 575;لأمثل مع أحدث إصدا= 585; من Microsoft Internet Explorer.

إذا أردت المتابعة عل= 09; أية حال، انق= 585; هنا.

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= ‹التار&= #1610;خ/الوقت› =
‹تذ&= #1610;يل الصفحة›
‹#›
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------=_NextPart_01C56DF5.994A5DD0 Content-Location: file:///C:/D91A186E/DRMOUSSABARQAWI-ACTUALSITUATIOPNOFTHALASSEMIAINJORDAN.files/master88.xml Content-Transfer-Encoding: quoted-printable Content-Type: text/xml; charset="utf-8" ------=_NextPart_01C56DF5.994A5DD0 Content-Location: file:///C:/D91A186E/DRMOUSSABARQAWI-ACTUALSITUATIOPNOFTHALASSEMIAINJORDAN.files/pres.xml Content-Transfer-Encoding: quoted-printable Content-Type: text/xml; charset="utf-8" ------=_NextPart_01C56DF5.994A5DD0 Content-Location: file:///C:/D91A186E/DRMOUSSABARQAWI-ACTUALSITUATIOPNOFTHALASSEMIAINJORDAN.files/slide0001.htm Content-Transfer-Encoding: quoted-printable Content-Type: text/html; charset="us-ascii" ACTUAL SITUATIOPN OF THALASSEMIA IN JORDAN
ACTUAL SITUATIOPN= OF THAL= ASSEMIA IN JORDAN
P= RESENTED BY:=
DR M= OUSSA BARQAWI
CONS= ULTANT PEDIATRICIAN / HEMATOLOGIST -ONCO= LOGIST
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INTRODUCTION
lB-Thalassemia and other Hemoglobinopathies (mainly sickle cell disease ) are common gen= etic disease in Jordan.
l
lmore than 1000 patients are registered
l
lWith a carriers rate between 3-6% &#= 13;
l
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charset="us-ascii" ACTUAL SITUATIOPN OF THALASSEMIA IN JORDAN
DISTRIBUTION OF PATIENTS OVER THE DIFFERENT REGIONS
l1-Is variable
l2-The majorities are in Amman, north of Jordan and the valley of Jordan
l<= span lang=3DEN-US style=3D'font-family:"Times New Roman";mso-ascii-font-family:= "Times New Roman"; mso-bidi-font-family:"Times New Roman";mso-hansi-font-family:"Times New Ro= man"; mso-ansi-language:EN-US'>3- There are 5 Thalassemic centers In Jordan <= /b>where patients are registered <= /span>
l4- the remaining patients are followed in the = different hospitals ,of the ministry of health= , royal medical services ,universities hospital = and private hospitals. <= /div>
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Distributions Of The Patients In Jordan
l60% of the patients in central Jordan which include Amman , Zarqa = , and sult
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charset="us-ascii" ACTUAL SITUATIOPN OF THALASSEMIA IN JORDAN
Patients Follow UP Distributions
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ØAmira Rahma hospital thalassemia center)-Irbid:219
ØZarka Hospital Thalass= emia Center  :90
ØGhor Alsafi Thalassemia Center:30
ØAjloun Thalassemia Cen= ter:?
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file:///C:/D91A186E/DRMOUSSABARQAWI-ACTUALSITUATIOPNOFTHALASSEMIAINJORDAN.files/slide0006.htm Content-Transfer-Encoding: quoted-printable Content-Type: text/html; charset="us-ascii" ACTUAL SITUATIOPN OF THALASSEMIA IN JORDAN
Age distribution of Patients in AlBashir Hos= pital
10
> 25 years<= span style=3D'mso-spacerun:yes'>        = ;        
58
20-25 years        = ;      
54
15-20 years        = ;      
88
10-15 years        = ;      
77
5-10 years        = ;        
28
0-5 years        = ;         
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= Age Distribution of Sickle Cell Disease and Sic= kle Thalassemia in Al Bashir Hospital
1
>25 years    
16
20-25 years 
30
15-20 years 
27
10-15 years 
14
5-10 years   
7
0-5 years     
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Age distribution of patients in Amira Rah= ma Thalassemia Center
21
>20 years
34
15-20 years
58
10-15 years
58
5-10 years
21
0-5 years
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= Age Distribution of Sickle Cell Disease and Sic= kle Thal in Amira Rahma Hospital
1
>20 years
1
15-20 years
5
10-15 years
11
5-10 years
9
0-5 years
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Age Distribution of Patient in Zarka Tha= lassemia Center
0
>20 years
15-20 years
18
10-15 years
37
5-10 years
23
0-5 years
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Age Distribution of Sickle Cell Disease and Sickle/Thal in Zarka Hospital
0
15-20 years
0
>20 years
4
10-15 years
3
5-10 years
2
0-5 years
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Consanguinity in patient’s families
27%
l No consanguinit= y
26%
l Second and Thir= d degree consanguinity
47%
l First degree consanguinity<= /span>
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G= enetic Aspect
lMolecular defects in Jordan were studied and identified by Dr. Alkhatib and Qubbaj of Jordan University which show the following: <= span lang=3DAR-JO style=3D'font-size:83%;mso-ansi-language:EN-US;display:none'>=
l
=
IVS II-1 (G-A)<= b>
7% of mutations are
C37 (TGG-TGA)
7.7 % of mutat= ions are
IVS-I-6 (T-C)<= b>
8.5% of mutati= ons are
IVS-II-745 (C-<= /span>G)
15.5% of mutat= ions are
IVS-I-110 (G-<= span lang=3DEN-US style=3D'mso-bidi-language:AR-SA'>A )<= b>
15.5 % of mutations are
IVS-I-1 (G-A)<= b>
17% of mutations are <= b>
<= ![endif]>
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Care and Treatment given for Thalassemic patients in Jordan=
l= Treatment of thalassemia, as other chronic blood diseases, is completely free of charge and covered by the ministry of health.
lThis treatment includes:
1)Hyper trans= fusion regimen (RBC’s transfusion given every 3-4 weeks to keep Hb level above 9.5 gr/dl) Washed RBCR= 17;s = are given for patients in Albashir center and Irbid center= , otherwise packed RBC’s are given in other places.= 3;
vBefore every transfusion, patients are screened for antibo= dies (to detect alloimmunisation)
vTransfused blood is screened for hepatitis B and C viruses= , for HIV virus, and syphilis.
v  =
<= ![endif]>
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2.Chelating therapy with Desferioxamine (20-40 mg / <= /span>kg body weight) daily over night by subcutaneous infusion for every patients with ferritin level over 1000 ug.
qInfusion pump is given free of charge (by ministry of <= /b>health and Novartis company)
qVitamin C (2-3 mg / kg orally) given with every desferrioxamine injection
qSyringes and scalp vein needles are given free of charg= e
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&#= 13;
&Osla= sh; Hypersplenism.
Ø
ØAbdominal discomfort.
Ø
= 3. Splenectomy when indicated
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